Iranian Journal of Radiology

Published by: Kowsar

Extensive Gastroesophageal Varices in a Non-Cirrhotic Female with Left Isomerism: A Case Report and Literature Review

Maryam Rahmani 1 , Faeze Salahshour 1 , * , Reza Taslimi 2 , Ali Borhani 1 and Sina Kianoush 3
Authors Information
1 Advanced Diagnostic and Interventional Radiology Research Center, Tehran University of Medical Sciences, Tehran, Iran
2 Department of Internal Medicine, Imam Khomeini Hospital, Tehran University of Medical Sciences, Tehran, Iran
3 The Johns Hopkins Ciccarone Center for the Prevention of Heart Disease, Baltimore, Maryland, USA
Article information
  • Iranian Journal of Radiology: April 2017, 14 (2); e34656
  • Published Online: June 1, 2016
  • Article Type: Case Report
  • Received: November 24, 2015
  • Revised: February 15, 2016
  • Accepted: March 14, 2016
  • DOI: 10.5812/iranjradiol.34656

To Cite: Rahmani M, Salahshour F, Taslimi R, Borhani A, Kianoush S. Extensive Gastroesophageal Varices in a Non-Cirrhotic Female with Left Isomerism: A Case Report and Literature Review, Iran J Radiol. 2017 ; 14(2):e34656. doi: 10.5812/iranjradiol.34656.

Copyright © 2016, Tehran University of Medical Sciences and Iranian Society of Radiology. This is an open-access article distributed under the terms of the Creative Commons Attribution-NonCommercial 4.0 International License ( which permits copy and redistribute the material just in noncommercial usages, provided the original work is properly cited.
1. Introduction
2. Case Presentation
3. Discussion
  • 1. Gayer G, Apter S, Jonas T, Amitai M, Zissin R, Sella T, et al. Polysplenia syndrome detected in adulthood: report of eight cases and review of the literature. Abdom Imaging. 1999; 24(2): 178-84[PubMed]
  • 2. Murray CP, Yoo SJ, Babyn PS. Congenital extrahepatic portosystemic shunts. Pediatr Radiol. 2003; 33(9): 614-20[DOI][PubMed]
  • 3. Niwa T, Aida N, Tachibana K, Shinkai M, Ohhama Y, Fujita K, et al. Congenital absence of the portal vein: clinical and radiologic findings. J Comput Assist Tomogr. 2002; 26(5): 681-6[PubMed]
  • 4. Kobayashi N, Niwa T, Kirikoshi H, Fujita K, Yoneda M, Saito S, et al. Clinical classification of congenital extrahepatic portosystemic shunts. Hepatol Res. 2010; 40(6): 585-93[DOI][PubMed]
  • 5. Alonso-Gamarra E, Parron M, Perez A, Prieto C, Hierro L, Lopez-Santamaria M. Clinical and radiologic manifestations of congenital extrahepatic portosystemic shunts: a comprehensive review. Radiographics. 2011; 31(3): 707-22[DOI][PubMed]
  • 6. Koc Z, Oguzkurt L. Interruption or congenital stenosis of the inferior vena cava: prevalence, imaging, and clinical findings. Eur J Radiol. 2007; 62(2): 257-66[DOI][PubMed]
  • 7. Koc Z, Ulusan S, Oguzkurt L, Serin E. Symptomatic interrupted inferior vena cava: report of a case presenting with haematochezia. Br J Radiol. 2007; 80(954)-4[DOI][PubMed]
  • 8. Slosman F, Schmid MR, Pfammatter T. Agenesis of the hepatic segment of the inferior vena cava with portal continuation. AJR Am J Roentgenol. 2001; 177(1): 120-2[DOI][PubMed]
  • 9. Chevallier P, Peten EP, Marcy PY, Fabiani P, Diaine B, Padovani B. Inferior vena cava hypoplasia with intrahepatic venous continuation: sonographic, angiographic and MR features including MR angiography. Clin Imaging. 1999; 23(2): 99-102[PubMed]
  • 10. Bercoff E, Colin R, Benozio M, Janvresse A, Berland J, Fillastre JP. Infrahepatic interruption of the inferior vena cava with portal continuation. Radiology. 1985; 154(3): 771-2[DOI][PubMed]
  • 11. Balkanci F, Ozmen MN. Case report: interruption of the inferior vena cava with anomalous intrahepatic continuation. Br J Radiol. 1993; 66(785): 457-9[DOI][PubMed]
  • 12. Ghossain MA, Haddad SN, Aoun NJ, Atallah NG, Jebara VA, Moussally AS, et al. Portal and hemiazygos continuation of the inferior vena cava: report of an unusual case. Br J Radiol. 1988; 61(724): 333-4[DOI][PubMed]
  • 13. Minniti S, Visentini S, Procacci C. Congenital anomalies of the venae cavae: embryological origin, imaging features and report of three new variants. Eur Radiol. 2002; 12(8): 2040-55[DOI][PubMed]
  • 14. Kandpal H, Sharma R, Gamangatti S, Srivastava DN, Vashisht S. Imaging the inferior vena cava: a road less traveled. Radiographics. 2008; 28(3): 669-89[DOI][PubMed]
  • 15. Mathews R, Smith PA, Fishman EK, Marshall FF. Anomalies of the inferior vena cava and renal veins: embryologic and surgical considerations. Urology. 1999; 53(5): 873-80[PubMed]
  • 16. Yigit H, Yagmurlu B, Yigit N, Fitoz S, Kosar P. Low back pain as the initial symptom of inferior vena cava agenesis. AJNR Am J Neuroradiol. 2006; 27(3): 593-5[PubMed]
  • 17. Paksoy Y, Gormus N. Epidural venous plexus enlargements presenting with radiculopathy and back pain in patients with inferior vena cava obstruction or occlusion. Spine (Phila Pa 1976). 2004; 29(21): 2419-24[PubMed]
  • 18. Jeong HJ, Seo IY, Rim JS. Chronic post-thrombotic obstruction of the inferior vena cava: both renal veins being the cause of painless gross hematuria from pelviureteral mucosal varices in normal functioning kidney. Yonsei Med J. 2003; 44(6): 1119-21[DOI][PubMed]
  • 19. Sonin AH, Mazer MJ, Powers TA. Obstruction of the inferior vena cava: a multiple-modality demonstration of causes, manifestations, and collateral pathways. Radiographics. 1992; 12(2): 309-22[DOI][PubMed]
  • 20. Dahan H, Arrive L, Monnier-Cholley L, Le Hir P, Zins M, Tubiana JM. Cavoportal collateral pathways in vena cava obstruction: imaging features. AJR Am J Roentgenol. 1998; 171(5): 1405-11[DOI][PubMed]
  • 21. Kapur S, Paik E, Rezaei A, Vu DN. Where there is blood, there is a way: unusual collateral vessels in superior and inferior vena cava obstruction. Radiographics. 2010; 30(1): 67-78[DOI][PubMed]
  • 22. Albrechtsson U. The portal vein as collateral in inferior vena cava obstruction. Cardiovasc Radiol. 1979; 2(2): 107-10[PubMed]
  • 23. Wedig MP, Stark GB. [Upper gastrointestinal hemorrhage due to vena cava obstruction]. Z Kinderchir. 1990; 45(6): 379-82[DOI][PubMed]
  • 24. Maunoury V, Plane C, Ernst O, Seguy D, Quandalle P. [Absence of subrenal inferior vena cava revealed by rupture of duodenal varices in an adult]. Gastroenterol Clin Biol. 1994; 18(10): 889-91[PubMed]
  • 25. Zhou H, Janssen D, Gunther E, Pfeifer U. Fatal bleeding from duodenal varices as a late complication of neonatal thrombosis of the inferior vena cava. Virchows Arch A Pathol Anat Histopathol. 1992; 420(4): 367-70[PubMed]
Creative Commons License Except where otherwise noted, this work is licensed under Creative Commons Attribution Non Commercial 4.0 International License .

Search Relations:



Create Citiation Alert
via Google Reader

Readers' Comments