Intraosseous Neurofibroma and Concurrent Involvement of the Mandible, Maxilla and Orbit: Report of a Case

AUTHORS

Zahra Dalili 1 , * , Gholamhossein Adham 2

1 Department of Maxillofacial Radiology, Dental School, Guilan University of Medical Sciences, Dalili@gums.ac.ir, Iran

2 Department of Maxillofacial Surgery, Dental School, Guilan University Of Medical Sciences, Iran

How to Cite: Dalili Z , Adham G . Intraosseous Neurofibroma and Concurrent Involvement of the Mandible, Maxilla and Orbit: Report of a Case, Iran J Radiol. Online ahead of Print ; 9(1):45-9. doi: 10.5812/iranjradiol.6684.

ARTICLE INFORMATION

Iranian Journal of Radiology: 9 (1); 45-9
Published Online: March 25, 2012
Article Type: Case Report
Received: December 27, 2010
Accepted: December 21, 2011
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Abstract

Neurofibroma is an autosomal dominant disorder which has major criteria such as hyperpigmentation (cafe-au lait spots), cutaneous and subcutaneous tumors and bone deformities. In this report, a case of multifocal intraosseous neurofibroma in a 16-year-old male with right facial asymmetry, multiple unerupted maxillary posterior teeth and a previous history of infratemporal and orbital neurofibroma is presented. The majority of reported cases occurred in the posterior portion of the mandible and a limited number in the maxilla. Cone beam CT (CBCT) was performed for better evaluation of the extension and form of the maxillary and mandibular lesions. This report presents a rare situation of simultaneous peripheral neurofibromatosis (NF) and multifocal intraosseous NF in the mandible, maxilla and orbits and also focuses on advanced imaging findings of bony and soft tissue neurofibroma.

© 2012, Author(s). This is an open-access article distributed under the terms of the Creative Commons Attribution-NonCommercial 4.0 International License (http://creativecommons.org/licenses/by-nc/4.0/) which permits copy and redistribute the material just in noncommercial usages, provided the original work is properly cited.

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